FAQs about Moyamoya Disease

How can I schedule an appointment?
Email us at neuro@nshs.edu, call us at (516) 562-3023 or (516) 562-3064 or fill out our Request an Appointment form.

What is Moyamoya disease?
Moyamoya disease is a vascular disease of the brain characterized by progressive blockage of the large branches of the internal carotid artery of the brain.  Patients present with symptoms related to this vessel blockage resulting in stroke, transient neurologic deficit and seizure.

Who gets Moyamoya disease? 
Moyamoya disease is most commonly seen in patients of Asian descent, however, patients of all races can develop the disease. It is most commonly seen in children and young adults.

What are the treatments?  
The only treatment that is reliable is surgical revascularization of the brain utilizing either an indirect or direct vascular graft (see above).
 

What is the procedure for diagnosis and treatment?

• Diagnostics. Patients are evaluated by our clinical staff and then are required to complete a three component diagnostic evaluation including Hemispheric perfusion imaging, MRI and MRA with NOVA vessel flow testing and diagnostic angiography.
• Conferencing. Patient's testing is reviewed in Moyamoya conference held twice per month.  Results of diagnostic testing are reviewed in our multidisciplinary conference and treatment recommendation is made.
• Treatment. Patients are recommended to undergo either surgical revascularization or medical therapy.
• Follow up. Surgical patients require follow-up MRA imaging at 3 months and angiography at 6 months.  Medical patients have their follow up tailored to their unique presentation and subsequent symptom pattern.
   

What will I receive after my consultation?
Each patient receives a podcast of his or her imaging with a full explanation of the treatment plan.